 |
Case Report
Epithelioid hemangioendothelioma of parapharyngeal space: A rare clinical entity
1 Senior Resident, Department of ENT, AIIMS, Patna, Bihar, India
2 Additional Professor, Department of ENT, AIIMS, Patna, Bihar, India
3 Associate Professor, Department of ENT, AIIMS, Patna, Bihar, India
4 Assistant Professor, Department of Pathology/Lab Medicine, AIIMS, Patna, Bihar, India
5 Senior Resident, Department of Pathology/Lab Medicine, AIIMS, Patna, Bihar, India
Address correspondence to:
Kranti Bhavana
Department of ENT, AIIMS Patna, Phulwarisharif, Patna 801507, Bihar,
India
Message to Corresponding Author
Article ID: 100071Z10DK2020
Access full text article on other devices
Access PDF of article on other devices
How to cite this article
Kumar D, Bhavana K, Bharti B, Kumar T, Tiwari P. Epithelioid hemangioendothelioma of parapharyngeal space: A rare clinical entity. J Case Rep Images Oncology 2020;6:100071Z10DK2020.ABSTRACT
Introduction: An epithelioid hemangioendothelioma is a rare vascular neoplasm primarily of lung, liver, and bones. It is regarded as a neoplasm of borderline or low-grade malignant potential uncommonly seen in head and neck region. It may manifest in other parts of body like breast, lymph nodes, mediastinum, brain, meninges, spine, skin, abdomen, and many other sites. Due to its heterogeneous presentation, rarity, and malignant potential, it is often misdiagnosed and not adequately treated.
Case Report: We herein present a case of hemangioendothelioma of parapharyngeal space in an adult male with progressive swelling in right cervical region. Involvement of parapharyngeal space by this tumor is very rare, which warrants reporting of this case. The dumbbell-shaped tumor was surgically excised in toto and histopathology confirmed the diagnosis.
Conclusion: A wide surgical excision and regular follow-up would be appropriate management. Further research and studies are needed to formulate standardized treatment protocols for this rare tumor.
Keywords: Epithelial hemangioendothelioma, Parapharyngeal neoplasm, Vascular neoplasm
SUPPORTING INFORMATION
Acknowledgments
We express our gratitude to the entire team of Department of ENT and Department of Pathology, AIIMS Patna, India.
Author ContributionsDheeraj Kumar - Conception of the work, Design of the work, Acquisition of data, Analysis of data, Drafting the work, Revising the work critically for important intellectual content, Final approval of the version to be published, Agree to be accountable for all aspects of the work in ensuring that questions related to the accuracy or integrity of any part of the work are appropriately investigated and resolved.
Kranti Bhavana - Conception of the work, Design of the work, Acquisition of data, Analysis of data, Drafting the work, Revising the work critically for important intellectual content, Final approval of the version to be published, Agree to be accountable for all aspects of the work in ensuring that questions related to the accuracy or integrity of any part of the work are appropriately investigated and resolved.
Bhartendu Bharti - Conception of the work, Design of the work, Drafting the work, Revising the work critically for important intellectual content, Final approval of the version to be published, Agree to be accountable for all aspects of the work in ensuring that questions related to the accuracy or integrity of any part of the work are appropriately investigated and resolved.
Tarun Kumar - Acquisition of data, Analysis of data, Drafting the work, Revising the work critically for important intellectual content, Final approval of the version to be published, Agree to be accountable for all aspects of the work in ensuring that questions related to the accuracy or integrity of any part of the work are appropriately investigated and resolved.
Prerna Tiwari - Acquisition of data, Analysis of data, Drafting the work, Revising the work critically for important intellectual content, Final approval of the version to be published, Agree to be accountable for all aspects of the work in ensuring that questions related to the accuracy or integrity of any part of the work are appropriately investigated and resolved.
Guarantor of SubmissionThe corresponding author is the guarantor of submission.
Source of SupportNone
Consent StatementWritten informed consent was obtained from the patient for publication of this article.
Data AvailabilityAll relevant data are within the paper and its Supporting Information files.
Conflict of InterestAuthors declare no conflict of interest.
Copyright© 2020 Dheeraj Kumar et al. This article is distributed under the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any medium provided the original author(s) and original publisher are properly credited. Please see the copyright policy on the journal website for more information.
