Case Report


Epithelioid angiosarcoma involving the small intestine in a 3-year-old with an unusual non-aggressive behavior: Case report and review of the literature

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1 Faculty of Medicine, University of Ottawa, Ontario, Canada

2 Department of Pathology, The Ottawa Hospital, Ottawa, Ontario, Canada

3 Department of Laboratory Medicine, Children’s Hospital of Eastern Ontario, Ottawa, Ontario, Canada

Address correspondence to:

Joseph de Nanassy

Pediatric Pathologist, Children’s Hospital of Eastern Ontario, 401 Smyth Rd, Ottawa, ON K1H 8L1,

Canada

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Article ID: 100079Z11YN2024

doi: 10.5348/100079Z11YN2024CR

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How to cite this article

Nasr Y, Chernetsova E, Tristani L, de Nanassy J. Calcifying fibrous tumor involving the paraspinal region of a child: A rare case report. J Case Rep Images Pathol 2024;10(2):12–16.

ABSTRACT


Malignant vascular lesions involving the gastrointestinal tract include but are not limited to, angiosarcoma, epithelioid and/or spindle cell hemangioendothelioma, and Kaposi sarcoma. Most epithelioid angiosarcomas (EASs) are reported in adult patients, with a male predominance. Epithelioid angiosarcomas arising in the gastrointestinal tract are rare, particularly in pediatric patients. We report a 3-year-old female patient presented by a Meckel’s diverticulum. Surgical excision revealed an epithelioid angiosarcoma of the small intestine. She received no additional chemotherapy or radiation after surgery as the patient’s parents refused. She was followed annually by imaging and was disease-free seven years after surgery.

Keywords: Epithelioid angiosarcoma, Meckel’s diverticulum, Neoplasia, Pediatric

SUPPORTING INFORMATION


Author Contributions

Youssef Nasr - Acquisition of data, Analysis of data, Drafting the work, Revising the work critically for important intellectual content, Final approval of the version to be published, Agree to be accountable for all aspects of the work in ensuring that questions related to the accuracy or integrity of any part of the work are appropriately investigated and resolved.

Elizaveta Chernetsova - Analysis of data, Drafting the work, Revising the work critically for important intellectual content, Final approval of the version to be published, Agree to be accountable for all aspects of the work in ensuring that questions related to the accuracy or integrity of any part of the work are appropriately investigated and resolved.

Lauren Tristani - Acquisition of data, Analysis of data, Drafting the work, Final approval of the version to be published, Agree to be accountable for all aspects of the work in ensuring that questions related to the accuracy or integrity of any part of the work are appropriately investigated and resolved.

Joseph de Nanassy - Conception of the work, Design of the work, Acquisition of data, Analysis of data, Drafting the work, Revising the work critically for important intellectual content, Final approval of the version to be published, Agree to be accountable for all aspects of the work in ensuring that questions related to the accuracy or integrity of any part of the work are appropriately investigated and resolved.

Guarantor of Submission

The corresponding author is the guarantor of submission.

Source of Support

None

Consent Statement

Written informed consent was obtained from the patient for publication of this article.

Data Availability

All relevant data are within the paper and its Supporting Information files.

Conflict of Interest

Authors declare no conflict of interest.

Copyright

© 2024 Youssef Nasr et al. This article is distributed under the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any medium provided the original author(s) and original publisher are properly credited. Please see the copyright policy on the journal website for more information.